Systemic mastocytosis in adults: update on diagnosis, risk stratification and management. Pardanani A(1). Author information: (1)Division.
Am J Hematol. Mar;90(3) doi: /ajh Systemic mastocytosis in adults: update on diagnosis, risk stratification, and management.
Disease overview:Systemic mastocytosis (SM) results from a clonal proliferation of abnormal mast cells (MC) in one or more extra‐cutaneous organs. Minor diagnostic criteria include elevated serum tryptase level, abnormal MC expression of CD25 and/or CD2, and presence of KITDV.